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Subacute Sclerosing Panencephalitis
Book chapter

Subacute Sclerosing Panencephalitis

J Gutierrez and C Singer
Encyclopedia of Movement Disorders, Three-Volume Set, pp.187-189

Abstract

Demyelinating disease CNS viral infection Early dementia Childhood myoclonus Chronic brain infection Subacute sclerosing panencephalitis (SSPE) CNS infection Periodic complexes Measles virus
Subacute Sclerosing Panencephalitis is a chronic, persistent viral infection of the central nervous system caused by the wild-type measles virus. The disease presents a few years after the primary measles infection with behavioral changes, usually followed by myoclonus, akinesia, mutism, vegetative state, and death.

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